Table 1 List of patients who had ADPKD and glomerular disease with biopsy-proven renal histopathology
Patient no. | First author (Ref. No.) | Age | Gender | Serum albumin (g/dL) | Cr (mg/dL) | Proteinuria (g/day) | Hematuria (/HPF) | Renal biopsy | Renal histopathology | Treatment | Follow-up period | Outcome |
|---|---|---|---|---|---|---|---|---|---|---|---|---|
1 | Murphy [4] | 44 | M | 3.4 | 9.9 | 7 | NA | O | FSGS | ACEi | 32 months | HD |
2 | Montoyo [5] | 35 | M | 2.4 | 3.5 | 14 | NA | O | FSGS | ACEi | 3 months | HD |
3 | Dionisio [6] | 58 | M | NA | Slight increase | 8 | NA | O | FSGS | Steroid, ACEi | 6 years | HD |
4 | Contreas [3] | 65 | F | 3.7 | 1.2 | 5.8 | NA | O | FSGS | ACEi | 3 years | CCr 32 ml/min, proteinuria 5.5 g/day |
5 | Shikata [7] | 53 | F | 2.2 | 1.0 | 6 | 3-5 | O | MN | Pred, | NA | NA |
6 | Saxena [8] | 22 | M | 2.5 | 0.8 | 6 | occasional | NA | MN | NA | NA | NA |
7 | Peces [9] | 38 | M | NA | 1 | 11.8 | NA | P | MN | ARB, Pred, MMF | 10 years | CCr 114 ml/min, proteinuria 0.4 g/day |
8 | Nakahama [10] | 14 | M | 1.7 | CCr 114 ml/min | 23.0 | A few | P | MCD | MP, Pred | 1 months | Remission |
9 | Kuroki [11] | 18 | F | 3.4 | 0.9 | 5.4 | 0 | O | MCD | Pred, CPA | 6 months | Remission |
10 | Panisello [12] | 67 | M | 4.4 | 6.3 | 4.2 | 10 | O | IgAN | NA | 3 months | Cr 9.2 mg/dL |
11 | Hiura [13] | 70 | M | 2.2 | 1.69 | 5.76 | >100 | O | IgAN | Pred | 5 years | CCr 40.9 ml/min, proteinuria 0.08 g/day |
12 | D’Cruz [14] | 35 | M | 3.0 | 1.7 | 4.67 | 8-10 | O | PIGN | ARB | 12 weeks | Remission |
13 | Villar [15] | 28 | M | NA | 5.7 | 4.7 | NA | O | PIGN | ACEi | 1 year | PD |
14 | Villar [15] | 25 | M | 2.7 | 5.5 | 12 | NA | O | MPGN | MP | 10 months | PD |
15 | Seyrek [16] | 56 | F | NA | NA | 0.5 | many | NA | MesGN | Pred | 1 year | Remission |
16 | Hariharan [17] | 44 | M | 2.5 | 1.35 | 11 | 10-12 | P | IDGS | NA | 1 year | HD |
17 | Licina [18] | 69 | F | NA | 5 | (3+) | Many | O | CrGN | MP, Pred | 3 months | Cr 2.4 mg/dL |
18 | Present case 1 | 60 | F | 3.7 | 4.5 | 2.03 | >100 | P | ANCA-associated CrGN | MP, Pred | 21 months | Cr 2.8 mg/dL, proteinuria 0.2 g/day |
19 | Present case 2 | 54 | F | 3.0 | 5.7 | 3.85 | >100 | P | ANCA-associated CrGN | MP, Pred, PEX | 1 month | HD |