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Table 1 Demographic and clinical characteristics of 146 patients with aHUS

From: Turkish pediatric atypical hemolytic uremic syndrome registry: initial analysis of 146 patients

Male (%) / Female (%) 62 (42.4) / 84 (57.6)
Current age, years  
 Mean (SD) 7.98 (5.0)
 Median (IQR) 6.53 (3.8–11)
Age at diagnosis, years  
 Mean (SD) 4.82 (4.4)
 Median (IQR) 3.5 (1.2–7.4)
Age category (years) at the time of diagnosis, n (%)  
 <2 53 (36.3)
 2 to <5 40 (27.4)
 5 to <12 38 (26)
 ≥12 15 (10.3)
Duration of follow-up (years)  
 Mean (SD) 2.9 (2.5)
 Median (IQR) 2.1 (1.2–3.8)
Consanguinity (%) 42 (28.8)
Family history of aHUS (%) 7 (4.8)
Anuria (%) /oliguria at admission (%) 41 (28) / 67 (45.8)
Duration of anuria at admission (days)  
 Mean (SD) 6.3 (4.5)
 Median (IQR) 5 (2–10)
Duration of oliguria at admission (days)  
 Mean (SD) 6 (6.8)
 Median (IQR) 3 (2–7)
Extrarenal involvement, n (%) 61 (41.7)
 Central nervous system 41 (28.1)
 Gastrointestinal system 16 (10.9)
 Cardiac 9 (6.1)
 Respiratory system 10 (6.8)
Patients with GFR <90 mL/min/1.73 m2 at admission, n (%) 139 (95.2)
Hypocomplementemia (%)a 66 (48.5)
Renal biopsy at admission (%) 44 (30.1%)
  1. SD: standard deviation; IQR: interquartile range; aHUS: atypical hemolytic uremic syndrome; GFR: glomerular filtration rate. aData is available for 136 patients