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Table 1 Clinical features, pathology of the kidney and lymph nodes and treatments administered of 26 patients with KD-associated nephrotic syndrome

From: Nephrotic syndrome associated with Kimura’s disease: a case report and literature review

Reported by

Case

Country

Gender

Age

Urine protein

(g/24 h)

Serum albumin

(g/L)

Serum creatinine(umol/L)

Serum IgE

(IU/ml)

Eosinophils

(%)

Renal biopsy

Treatment

X W Xiao

1

China

Male

23

12.77

34.6

88

582

0.44

Mesangial proliferation

Steroid+TW

X F Zhang

2

China

Male

46

6

26.3

62.9

43.4

0.15

Minimal change disease

Steroid

P C Li

3

China

Male

49

10.07

15.7

75

 

0.27

Mesangial proliferation

Steroid

H Sun

4

China

Male

40

8.34

30.8

480

 

0.15

Acute tubular necrosis

Steroid

Y W Zhang

5

China

Male

23

6.05

23

 

2500

 

IgA nephropathy

Steroid+CTX

L L Shao

6

China

Male

42

0.27

 

131

1316

0.354

IgA nephropathy

MMF

J L Meng

7

China

Male

43

6

15.5

115

 

0.574

Membranous nephropathy

Steroid

R Duan

8

China

Male

19

 

39.9

944

3000

0.154

FSGS

Steroid

 

9

China

Femal

35

0.84

31.2

 

500

0.015

Mesangial proliferation

Steroid

C B Liu

10

China

Male

19

3.65

 

97.1

272

0.32

Membranous nephropathy

Steroid

 

11

China

Male

21

5.32

 

185

397

0.17

IgA nephropathy

Steroid+TW

 

12

China

Male

36

14.1

 

123.76

620

0.1

Membranous nephropathy

Steroid+CTX

 

13

China

Male

25

12.8

 

88.4

989

0.44

Mesangial proliferation

Steroid+TW

 

14

China

Male

14

8.65

 

53.04

172

0.056

Mesangial proliferation

Steroid+LEF

 

15

China

Male

44

7.28

 

44.2

107

0.168

Mesangial proliferation

Steroid+LEF

 

16

China

Male

53

6.99

 

176.8

160

0.122

Mesangial proliferation

Steroid+CTX

 

17

China

Male

48

5.27

 

79.56

1378

0.26

Membranous nephropathy

Steroid

Y G Sha

18

China

Male

5

3.5

20.6

30

2000

0.21

Mesangial proliferation

Steroid

Koich

19

Japan

Male

9

11.1

12

238

4981

0.48

Minimal change disease

Steroid

Fatih

20

Turkey

Male

21

17.3

10

256

1987

0.21

FSGS

Steroid+CsA

Deepak

21

Vietnam

Male

14

4

21

123

 

0.11

Mesangial proliferation

Steroid

Chan

22

China

Male

25

19.7

18

85

1918

 

Mesangial proliferation

Steroid

S L Zhu

23

China

Male

23

9.3

16

 

1510

0.485

FSGS

Steroid

Mohamed

24

Egypt

Male

50

8.9

9

212

 

0.2

Membranous nephropathy

Steroid+MMF

K Sud

25

India

Femal

24

4.1

15

160

  

Minimal change disease

Steroid

Surendra

26

India

Male

18

8.6

21

62

 

0.03

Mesangial proliferation

Steroid

  1. TW Tripterygium wilfordii, CTX Cyclophosphamide, MMF Mycophenolate mofetil, LEF Leflunomide, CsA Cyclosporine