Skip to main content

Table 2 Summary of Reported Cases of Non Randal Monoclonal Immunoglobulin Deposition Disease with Membranous Features

From: An IgA1-lambda-type monoclonal immunoglobulin deposition disease associated with membranous features in a patient with IgG4-related kidney disease: a case report

  

First author

age

sex

IEP

IF

EM

Aetiology

treatment

outcome

1

2003

Touchard [20]

48

M

no

IgG3λ

subepi, subendo, mes

Idiopathic

PSL, Melphalan

remission

2

2003

Evans [21]

81

F

n/a

IgG1κ

subepi

ML (B cell)

PSL, CY, Chlorambucil

dead

3

2004

Nasr [1]

63

F

IgGλ

IgG1κ

subepi, subendo, mes

Idiopathic

 

n/a

4

  

42

M

no

IgG1κ

subepi, subendo

Idiopathic

PSL

decreased proteinuria

5

2008

Komatsuda [2]

44

M

no

IgG3κ

subepi

Idiopathic

mPSL, PSL

decreased proteinuria

6

  

24

M

no

IgG3κ

subepi, subendo, mes

Idiopathic

PSL

decreased proteinuria

7

2010

Miura [15]

61

M

no

IgA1λ

subepi

HCV, cancer

Operation, Anti-tumor drug

no change

8

2010

de Seigneux [22]

62

F

IgGλ

IgG1λ

subepi, subendo

MGUS

Dexamethasone, Thalidomide

remission

9

  

n/a

n/a

no

IgG1κ

n/a

CLL

CY, Fludarabine

remission

10

  

n/a

n/a

no

IgG1κ

n/a

Unknown

PSL

ESRD

11

2011

Guiard [23]

n/a

n/a

IgGλ

IgG1λ

n/a

MM

PSL, Melphalan

remission

12

n/a

n/a

no

IgG2κ

n/a

Unknown

Rituximab

remission

13

  

n/a

n/a

no

IgG3κ

n/a

Unknown

PSL, CY

remission

14

  

n/a

n/a

no

IgG3κ

n/a

Unknown

Rituximab

decreased proteinuria

15

2012

Yamada [24]

63

M

no

IgG1λ

subepi

HCV

PSL, Mizoribine

decreased proteinuria

16

2012

Ito [25]

68

F

no

IgG3λ

subepi, mes

MPO-ANCA

PSL

remission

17

2013

Ohashi [26]

27

F

no

IgG2κ

subepi, mes

Idiopathic

PSL

remission

18

2014

Omokawa [16]

62

F

no

IgG4κ

subepi, mes

IgG4RD(lung)

mPSL, PSL

decreased proteinuria

19

2017

Present case

65

M

no

IgA1λ

subepi

IgG4RKD(TIN)

PSL

no change

  1. Abbreviations: CY cyclophosphamide, EM electron microscopic study, HCV hepatitis C virus infection, IEP immunoelectrophoresis, IF immunofluorescent study, IgG4RD IgG4 related disease, IgG4RKD IgG4 related kidney disease, mes mesangial area, MGUS monoclonal gammopathy of undetermined significance, ML malignant lymphoma, MM multiple myeloma, MPO-ANCA myeloperoxidase-anti-neutrophil cytoplasmic antibody, mPSL methylprednisolone, n/a: not available, PSL prednisolone, subendo subendothelial area, subepi subepithelial area, TIN tubulointerstitialnephritis