Population | Intervention | Comparison | Outcome | Study design |
---|---|---|---|---|
Children (< 18) with a confirmed diagnosis of ADPKD or at risk of ADPKD due to their family history | Ultrasonography Cranial imaging Blood Pressure monitoring Monitoring for albuminuria Therapeutics Genetic counselling | Any intervention compared with any other or no intervention | Mortality Hospitalisations Chronic Kidney Disease Cardiovascular disease Hypertension | Randomised controlled trials (RCT) Non-randomised studies if adjusted for key confounders (age, health at baseline, co-morbidities). |