From: A cross-sectional nationwide survey of congenital and infantile nephrotic syndrome in Japan
Finnish-type disease N = 33 | Non-Finnish-type without syndrome N = 26 | Non-Finnish-type with syndrome N = 24 | |
---|---|---|---|
Medicationsa | |||
Steroids | 3/29 (NR, 3) | 18/25 (NR, 11; PR, 4; CR, 3) | 8/24 (NR, 7; PR, 1) |
Immunosuppressants | 3/28 (CSA, NR, 2; PR, 1) | 12/25 (NR, 1; PR, 2; CR, 9) | 4/24 (NR, 4) |
Immunosuppressant therapy by response | CSA, NR CSA + MZB, NR CSA, PR | CSA + TAC + MZB, NR CSA, PR (n = 2) CSA, CR (n = 4) MZB, CR CSA + MZB, CR CSA + CP, CR CSA + MMF + RTX, CR CSA + MZB + RTX, CR | CSA, NR (n = 4) |
Complicationsa | |||
Thrombosis | 5/32 | 1/26 | 1/24 |
Infections | 19/32 | 7/26 | 9/24 |
Other | 8/32 | 9/26 | 11/24 |