Table 1 Characteristics of patients at baseline and clinical presentation
Characteristic | All patients (n = 26) |
|---|---|
Age at diagnosis, years (SD) | 44 (25) |
Median follow-up, months (IQR) | 30 (19–46) |
Gender, no. male (%) | 16 (62) |
Ethnicity, no. (%) | |
NZ European | 8 (31) |
Maori | 4 (15) |
Pacific Islander | 11 (42) |
Asian | 3 (12) |
Comorbidities, no. (%) | |
Hypertension | 14 (54) |
Type 2 diabetes | 4 (15) |
Chronic kidney disease | 4 (15) |
Cr at diagnosis, umol/L (IQR) | 210 (146–300) |
Proteinuria, mg/mmol (IQR) | 552 (293–983) |
Nephrotic syndrome at diagnosis (%) | 11 (42) |
Dialysis at diagnosis, no. (%) | 2 (8) |
Normal renal function at diagnosis (%) | 4 (15) |
Hematuria, no. (%) | |
Microscopic | 25 (96) |
Macroscopic | 1 (4) |
Complement levels, no. (%) | |
Normal | 8 (31) |
Isolated low C3 | 12 (46) |
Low C3 and C4 | 5 (19) |
Not done | 1 (4) |
Complement screen, no. (%) | |
Not done | 11 (42) |
C3NeF negative, Factor H normal | 14 (54) |
Factor H deficiency | 1 (4) |
Monoclonal gammopathy, no. (%) | |
None | 23 (88) |
MGUS | 1 (4) |
Myeloma | 2 (8) |