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Table 2 Data of the analysis of urinary amino acids on admission

From: Acquired Fanconi syndrome in patients with Legionella pneumonia

 

Normal range (mmol/day)

Patient 1

Patient 2

Taurine

322.2–5214.5

1318.6

272.5

Phosphoethanolamine

31.0–110.0

49

34.4

Urea

130.3–493.2

223.9

341.3

Aspartic acid

< 12.7

N.D.

6.1

Hydroxyproline

N.D.

N.D.

N.D.

Threonine

79.9–528.3

1530.2

380.7

Serine

208.8–1020.0

1529.6

478.3

Asparagine

60.7–372.3

747.4

393.6

Glutamic acid

11.3–42.7

30.1

15.5

Glutamine

207.0–1357.3

1071.2

170.3

Sarcosine

< 99.0

24.8

N.D.

α-Aminoadipic acid

16.7–118.6

52.4

34.4

Proline

N.D.

18.4

25.6

Glycine

652.1–3670.6

852.4

336.2

Alanine

141.2–833.9

839.3

538.6

Citrulline

13.5–55.6

63.4

N.D.

α-Aminobutylic acid

< 27.1

N.D.

N.D.

Valine

24.8–82.2

97

104.2

Cystine

23.7–170.9

226.2

101.3

Cystathionine

< 44.7

21

334.6

Methionine

< 20.2

11.5

15.5

Isoleucine

7.5–23.5

26.5

29.2

Leucine

24.6–89.3

95.5

96.3

Tyrosine

50.6–308.4

327.4

111.8

Phenylalanine

27.2–110.2

150.7

199.8

γ-Amino β-hydroxybutyric acid

N.D.

N.D.

N.D.

β-Alanine

< 153.0

58.4

9.4

β-Amino-iso-butyric acid

< 1623.9

151.8

288.5

γ-Aminobutyric acid

N.D.

N.D.

N.D.

Monoethanolamine

195.3–606.2

292.8

356.8

Homocystine

N.D.

N.D.

N.D.

Histidine

436.4–2786.5

1392

496.8

3-Methylhistidine

113.4–480.9

202.9

396

1-Methylhistidine

59.3–2816.2

821.2

16.7

Carnosine

< 87.6

N.D.

21.2

Anserine

< 231.4

49.4

N.D.

Tryptophan

20.7–150.7

156.7

59.2

Hydroxylysine

< 22.9

3.8

N.D.

Ornithine

6.9–43.9

46.3

151.4

Lysine

51.6–1639.6

794.9

148.1

Arginine

11.6–54.8

51.5

31.3

  1. Underlining indicates an abnormal value.
  2. N.D. means not detected.