Patient [ref] | Age (yr, sex) | Initial symptoms | Hb, g/dl | S-Cr, mg/dl | Anti-GBM Abs | ANCA type | Crescents, % | Treatment | F/U | Outcome | |
---|---|---|---|---|---|---|---|---|---|---|---|
onset F/U | |||||||||||
1 [14] | 17, f | URTI | ~ 6.0 | 12.5 | - | + | p/MPO | 90 | supportive | - | Death at presentation |
2 [15] | 12, f | - | 7.4 | 0.5 | 0.3 | + | p/MPO | 13 | MP, PE, CY | few weeks | Normal GFR |
3 [16] | 12, m | fever,rash, arthritis | 10.6 | 7.4 | 2.1 | + | p/MPO | >60 | PE, MP, CY Pdn, MMF | 18 mos | GFR 58.5 ml/min |
4 [17] | 4, f | epistaxis | n.a. | 2.7 | 0.8 | + | p/MPO | 62 | PE, MP, Pdn, CY | 9 mos | Normal GFR |
5 [18] | 8, f | sore throat | 2.8 | 7.7 | - | - | p/MPO | 83 | supportive | - | Death at presentation |
6 [6] | 13, m | rash, sinusitis | n.a. | D | D | + | c/PR3 | + | PE, Pdn, CY | n.a. | ESRD |
7 [6] | 17, f | n.a. | D | D | + | p/MPO | 20 | PE, CY, Pdn, Aza | n.a. | ESRD | |
8 [this report] | 10, f | fever, malaise, legs pain | 4.4 | 0.53 | 0.66 | ± | p/MPO | 16 | MP, CY, Pdn, MMF | 10 mos | Normal GFR |