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Table 1 Laboratory data on admission

From: Isolated thrombotic microangiopathy of the small intestine in a patient with atypical hemolytic uremic syndrome – a case report

Parameter

Patient Value

Reference

ADAMTS13

 ADAMTS-13-antibodies (U/mL)

1.8

< 12

 ADAMTS-13-activity (IU/mL)

1.09

0.4–1.3

 ADAMTS-13-antigen (IU/mL)

0.38

0.41–1.41

Complement

 Complement classical pathway (%)

0,79

74–151

 Complement alternative pathway (%)

1,11

60–140

 Complement C3 (mU/L)

16

< 40

 sC5b-9 terminal Membrane attack complex (ng/mL)

184

58–239

Hematology

 Hemoglobin (g/dl)

11.3

11,8-15,5

 Platetlet count (×  103/μl)

290

160–400

 White blood cell count (/μL)

6.92 × 103

4–11

 Schistocyte-Count

< 0.1

 

Blood chemistry

 Lactate dehydrogenase (U/L)

565

< 250

 Haptoglobin (mg/L)

309

300–2000

 C-reactive protein (mg/L)

16.5

< 5

 Total serum bilirubin (mg/dl)

0.4

< 1.1