Table 1 Clinical characteristics of suspected ARPKD patients from Oman
From: Clinical and genetic characteristics of autosomal recessive polycystic kidney disease in Oman
| Â | N | % |
|---|---|---|
ARPKD patients | 40 | 100 |
Males | 19 | 48 |
Females | 21 | 53 |
Age at diagnosis: | ||
 Prenatal | 8 | 20 |
 Birth-1st month | 6 | 15 |
 2–12 months | 15 | 37.5 |
 1–8 years | 9 | 22.5 |
 > 8 years | 2 | 5 |
Clinical Features: | ||
 Systemic hypertension | 29 | 72.5 |
 Congenital hepatic fibrosis | 31 | 77.5 |
 Splenomegaly | 19 | 47.5 |
 Pulmonary hypoplasia | 7 | 17.5 |
 Perinatal deaths (<  28 days) | 4 | 10 |
 Postneonatal deaths (28 days - 1 year) | 2 | 5 |
 Chronic Kidney Disease | 24 | 60 |
 End Stage Kidney Disease | 12 | 30 |