Table 1 Clinical features of the seven late-onset OMN cases
Case No. | Case 1 | Case 2 | Case 3 | Case 4 | Case 5 | Case 6 | Case 7 |
|---|---|---|---|---|---|---|---|
Sex; Age (years) | M; 28 | Â F; 19 | M; 26 | Â F; 27 | M; 24 | Â F; 38 | M; 24 |
BMI (kg/m2) | 20.2 | 21.0 | 23.24 | 19.4 | 20.53 | 22.03 | 21.26 |
Complaint | Â | ||||||
 PrU | Yes | Yes | Yes | No | Yes | Yes | Yes |
 Elevated Scr | No | Yes | No | Yes | Yes | Yes | No |
BP (mmHg) | 110/80 | 110/70 | 130/80 | 110/70 | 130/70 | 110/85 | 120/80 |
Albumin (g/L) | 42.3 | 46.9 | 45.5 | 45.4 | 39.0 | 37.5 | 48.8 |
PrU (g/d)/UV (mL/d) | 0.83/2200 | 0.10/1660 | 0.95/1800 | 0.21/1930 | 0.88/2750 | 0.22/1830 | 0.31/2400 |
HeU | NEG | NEG | NEG | NEG | Trace | NEG | NEG |
Scr (µmol/L) | 135.2 | 116.9 | 95.1 | 128.7 | 152.2 | 227.1 | 131.1 |
*PrU (g/d) | 0.84–1.5 | 0.1–0.18 | NA | NEG to 0.21 | 0.88–2.0 | 0.22–1.73 | NA |
*Scr (µmol/L) | 130–147 | 107–184 | NA | 112–140 | 152–160 | 179–240 | 123–131 |
eGFR(mL/min/1.73m2) | 63.0 | 60.0 | 98.0 | 49.1 | 54.4 | 21.3 | 65.1 |
Ccr (ml/min) | 89.5 | 41.5 | NA | 58.3 | 74.4 | 29.1 | 63.8 |
Complement 3 (g/L) | NA | 0.82 | 1.32 | 0.61 | NA | 0.48 | 0.80 |
MAU (mg/L) | 1300 | 36 | NA | 48 | 291 | 64 | 239 |
TFU (mg/L) | 83.7 | < 2 | NA | 4.2 | 7.4 | 2.27 | 9.95 |
NAG (U/L) | 44 | 21 | NA | 9.2 | 3.3 | 3.3 | 10.9 |
α1M (mg/L) | 52.9 | 36 | NA | 82.5 | 15.3 | 9.53 | 77.4 |
IGU (mg/L) | NA | 9.21 | NA | 6.44 | 6.35 | 11.1 | 36.8 |
Sizek (cm*cm*cm)/ cortical thickness(cm) | Â | ||||||
 RK | 9.4*4.3*3.2/1.6 | 10.6*4.7*4.7/1.2 | 8.0*4.9*4.5/1.5 | 11.5*4.1*3.7/1.5 | 10.0*4.9*4.7/1.7 | 10.6*5.4*4.8/1.5 | 10.5*5.6*4.8/1.4 |
 LK | 10.9*4.7*3.6/1.7 | 12.2*5.2*4.6/1.5 | 8.4*5.3*4.4/1.8 | 11.7*4.5*4.4/1.6 | 11.2*4.8*4.2/1.7 | 9.7*4.8*4.5/1.7 | 11.6*6.2*5.1/1.6 |
Duration of illness/ follow up(months) | 3/NA | 89/77 | 3/NA | 27/NA | 24/NA | 20/2 | 6/NA |