From: Atypical haemolytic uremic syndrome with refractory multiorgan involvement and heterozygous CFHR1/CFHR3 gene deletion
Test
Value
Normal Range
ADAMTS-13 activity
58%
40–130%
C3
1.17Â g/L
0.79–1.52 g/L
C4
0.25Â g/L
0.16–0.38 g/L
C5
 > 200 mg/mL
100–169 mg/mL
C6
100Â mg/L
45–96 mg/L
C7
110Â mg/L
55–85 mg/L
C9
500Â mg/L
125–265 mg/L