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Table 2 Summary of reported cases of PGNMID with discrepancy between serum and glomerular deposits

From: Discordance of light chain isotypes between serum and glomerular deposits in proliferative glomerulonephritis with monoclonal IgG deposits: a case report and review of the literature

 

Article

Age

Sex

Cr (mg/dl)

eGFR (ml/min/1.73m2)

Proteinuria (g/gCr)

Glomerular deposition

FLC κ (mg/dl)

FLC λ (mg/dl)

Circulating paraprotein (method of detection)

Histological pattern

1

Redondo-Pachón 2012

76

M

3.4

18

11

IgG-λ

ND

ND

IgA-λ (sPEP) IgA-λ (uPEP)

MPGN

2

Batal 2014 pat 4

61

M

1.8

39

ND

IgG1-κ

ND

ND

IgM-λ (sIFE)

MPGN

3

Batal 2014 pat 7

44

F

ND

ND

ND

IgA-κ

ND

ND

IgG-κ (sIFE)

Mes GN

4

Vignon 2017 pat 1

ND

ND

ND

ND

ND

IgA-κ

ND

ND

IgA-λ (sIFE) λ (uIFE)

Mes GN

5

Vignon 2017 pat 5

ND

ND

ND

ND

ND

IgA-λ

35

36

IgA-κ (Western)

Mes GN

6

Shimohata 2017

76

M

3.6

17

4.9

IgG1-λ

ND

ND

IgG-κ (sPEP) IgG-κ (uPEP)

MN

7

Gumber 2018 pat 8

65

M

2

34

9.52

IgM-κ

ND

ND

IgG-κ IgG-λ (sPEP)

MPGN

8

Rosenstock 2021 pat 2

25

F

1.4

54

0.296

IgG1-κ

ND

ND

λ (sIFE)

Mes GN

9

The present case

50

M

0.98

54.3

0.84

IgG3-λ

213

74.2

IgG-κ (sIFE) BJP-κ (uIFE)

MN

  1. BJP Bence Jones protein, Cr Creatinine, eGFR Estimated glomerular filtration rate, F Female, FLC Free light chain, IgG Immunoglobulin G, M Man, ND Mes GN, Mesangial proliferative glomerulonephritis, MN Membranous nephropathy, MPGN Membranoproliferative glomerulonephritis, no data, pat patient, sIFE Serum immunofixation, sPEP Serum protein electrophoresis, uIFE Urine immunofixation, uPEP Urine protein electrophoresis